This is a defect by birth where there is a hole in the heart between the lower chambers (pumping chambers) of the heart. In addition the passage of blood to the lungs for oxygenation is obstructed completely resulting in a mixing of pure and impure blood, resulting in very blue babies.
Often this condition has to be palliated with a BT SHUNT in the first month of life itself and subsequent surgeries are required to obtain complete correction of this problem.
Once corrected this leads to normal life style. But the child has to be followed up carefully over the years to monitor the right ventricular function.
Sometimes the defect is more complex, with the passage to the lung being completely undeveloped and blood reaches the lung for oxygenation through alternate channels called Major Aorto Pulmonary Collateral Artery (MAPCA), since these channels come in a haphazard manner they need to be surgically connected together by a procedure called unifocalization and then connected to the right ventricle of the heart by a tube to recreate the pulmonary artery. For this the part taken and preserved from the heart of a heart donor called as homograft is used.